A single arterial trunk arises from the base of the heart giving rise to both pulmonary and systemic circulations.
Pathophysiology
Cyanotic defect resulting in delivery of inadequately oxygenated blood.
Single arterial trunk from the base of heart gives rise to the pulmonary artery, aorta, and coronary circulation.
Accompanied by unrestrictive VSD and single semilunar valve.
Type of truncus is differentiated by the existence and location of the main pulmonary artery and branch PA's.
Type I: Short MPA segment arises from trunk then branches into right and left PA.
Type II: PA's arises seperately from trunk but in close proximity. No MPA
Type III: PA's arises seperately from trunk but at some distance. No MPA
Assessment
Poor feeding, diaphoresis, tachypnea, and cyanosis.
Symptoms and signs of congestive heart failure are probably more common findings than cyanosis in patients presenting early in life.
Management
IV, O2, Monitor.
3cc/kg/hr D10W for infants under 1 year of age, D5W if over 1 year.
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